Classic case of cleidocranial dysplasia with an infected mandibular cyst

Introduction: Patients with cleidocranial dysplasia commonly present with significant dental problems, such as retention of multiple deciduous teeth, impaction or delayed eruption of teeth and the presence of multiple Madhu P. Sivan1, Jayakumar K.2, Jayalakshmi P. S.3, N. Sruthi4 Affiliations: 1MDS, Provisional Lecturer, Department of Oral and Maxillofacial Surgery, Government Medical College, Thrissur, Kerala State, India; 2MDS, Associate Professor and Head, Department of Oral and Maxillofacial Surgery, Government Medical College, Thrissur, Kerala State, India; 3MDS, Assistant Professor, Department of Oral and Maxillofacial Surgery, Government Medical College, Thrissur, Kerala State, India; 4BDS, Provisional Lecturer, Department of Oral and Maxillofacial Surgery, Government Medical College, Thrissur, Kerala State, India. Corresponding Author: Madhu P. Sivan, “Haritha”, Prasanthi Nagar, Kanattukara Post Office, Near Sree Kerala Verma College Ground, Thrissur, Kerala State, India680011; Email: [email protected] Received: 07 November 2016 Accepted: 19 December 2016 Published: 01 April 2017 supernumerary teeth. In fact, the presence of multiple supernumerary teeth is one among the pathognomonic triad for this condition; the other two being partial or complete absence of clavicles, and open sagittal sutures and fontanelles. This case report describes a patient having typical features of cleidocranial dysplasia who had to undergo surgical Enucleation and Debridement for an infected mandibular cyst. Factors dictating the treatment plan and the current trends in rehabilitation for such a patient have been discussed from a dental surgeon’s perspective acknowledging the shift in management paradigm for this condition over the years.